Doege-Potter Syndrome: A Presumptive Case of Metastatic Hemangiopericytoma with Persistent Hypoglycemia in a 27-Year-Old Male

Overview

Journal J ASEAN Fed Endocr Soc

Specialty Endocrinology

Date 2021 Jun 28

PMID 34177094

Citations 1

Authors

Von Lovel Zarra

Kenny Jun Demegillo

May Uyking-Naranjo

Ahmad Domado

Affiliations

Soon will be listed here.

Abstract

Doege-Potter syndrome (DPS) is a rare paraneoplastic condition characterized by hypoinsulinemic hypoglycemia from a solitary fibrous tumor. The underlying mechanism is the secretion of a prohormone form of insulin-like growth factor II (IGF-II) by the tumor, which causes decreased release of glucose into the circulation. We report the case of a 27-year-old Filipino male with presumptive DPS from a recurrent right temporo-zygomatic hemangiopericytoma (HPC). The complexity of DPS requires a multidisciplinary approach. Early screening for metastases from HPC may prevent the undesirable sequelae of the disease process.

Citing Articles

Paraneoplastic hypoglycemia: An overview for optimal clinical guidance.

Karamanolis N, Kounatidis D, Vallianou N, Alexandropoulos K, Kovlakidi E, Kaparou P Metabol Open. 2024; 23:100305.

PMID: 39185033 PMC: 11342107. DOI: 10.1016/j.metop.2024.100305.

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