Pseudohypoparathyroidism, Parkinsonism Syndrome, with No Basal Ganglia Calcification

Overview

Journal J Neurol Neurosurg Psychiatry

Publisher BMJ Publishing Group

Specialties Neurology
Neurosurgery
Psychiatry

Date 1988 May 1

PMID 3404168

Citations 5

Authors

B K Evans

D K Donley

Affiliations

Soon will be listed here.

Abstract

A 20 year old woman with pseudohypoparathyroidism, Parkinsonism and no basal ganglia calcifications shown by computed tomography is reported. She has typical features of pseudohypoparathyroidism and biochemical evidence of end-organ resistance to parathyroid hormone. She is mentally retarded and has tremor, rigidity, bradykinesia, and stooped posture. The cause of Parkinsonism in pseudohypoparathyroidism is thought to be basal ganglia calcification. This patient must have another pathophysiology, perhaps directly related to a G protein defect, causing impaired neurotransmission.

Citing Articles

Pseudohypoparathyroidism type 1B with involuntary movements: a case report and literature review.

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Parkinson's Disease and Metal Storage Disorders: A Systematic Review.

Botsford E, George J, Buckley E Brain Sci. 2018; 8(11).

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Pseudohypoparathyroidism with basal ganglia calcification: A case report of rare cause of reversible parkinsonism.

Song C, Zhao Z, Li W, Sun C, Liu Y Medicine (Baltimore). 2017; 96(11):e6312.

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Albright hereditary osteodystrophy: a case report.

Hugar D, Sajjanshetty S, Hugar S, Kadani M J Clin Diagn Res. 2014; 8(10):ZD28-30.

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Multiple intracranial calcifications and spinal compressions: rare complications of type la pseudohypoparathyroidism.

Tseng F, Su D, Chen H, Tsai K J Endocrinol Invest. 2005; 28(7):646-50.

PMID: 16218049 DOI: 10.1007/BF03347265.

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