Tuberous Sclerosis Complex: The Critical Role of the Interventional Radiologist in Management

Overview

Journal SA J Radiol

Specialty Radiology

Date 2021 May 3

PMID 33936797

Authors

Puneet Garg

Anuradha Sharma

Heena Rajani

Apratim R Choudhary

Rajkumar Meena

Affiliations

Soon will be listed here.

Abstract

Tuberous sclerosis complex (TSC) is an autosomal dominant neurocutaneous syndrome that is characterised by hamartomas in multiple organs, the characteristic imaging features of which are illustrated in this case report. Angiomyolipoma (AML) is the most common renal manifestation of TSC, which may present with life-threatening haemorrhage at the time of diagnosis. Interventional management with selective renal embolisation is currently the treatment of choice for the safe and effective management of ruptured renal AML.

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