» Articles » PMID: 33786104

Aortic Dissection in Familial Patients with Autosomal Dominant Polycystic Kidney Disease

Overview
Journal Ann Vasc Dis
Date 2021 Mar 31
PMID 33786104
Authors
Affiliations
Soon will be listed here.
Abstract

Autosomal dominant polycystic kidney disease (ADPKD) is the most common congenital kidney disease. However, reports on occasional cases of aortic dissection in PKD familial patients remain scarce. Herein, we describe rare aortic dissection cases in PKD familial patients (i.e., mother and daughter) and our successful treatment experience. The mother (84 years old) and daughter (53 years old) had a referral to us to treat type A acute aortic dissection. We performed emergency surgery and successfully treated the patients with an artificial graft. For comprehensive evaluation and treatment, ADPKD patients and their families should be screened for aortic diseases.

References
1.
Lumiaho A, Ikaheimo R, Miettinen R, Niemitukia L, Laitinen T, Rantala A . Mitral valve prolapse and mitral regurgitation are common in patients with polycystic kidney disease type 1. Am J Kidney Dis. 2001; 38(6):1208-16. DOI: 10.1053/ajkd.2001.29216. View

2.
Cornec-Le Gall E, Alam A, Perrone R . Autosomal dominant polycystic kidney disease. Lancet. 2019; 393(10174):919-935. DOI: 10.1016/S0140-6736(18)32782-X. View

3.
Silverio A, Prota C, Di Maio M, Polito M, Cogliani F, Citro R . Aortic dissection in patients with autosomal dominant polycystic kidney disease: a series of two cases and a review of the literature. Nephrology (Carlton). 2014; 20(4):229-35. DOI: 10.1111/nep.12373. View

4.
Schrier R, McFann K, Johnson A . Epidemiological study of kidney survival in autosomal dominant polycystic kidney disease. Kidney Int. 2003; 63(2):678-85. DOI: 10.1046/j.1523-1755.2003.00776.x. View

5.
Zhou Z, Xu Y, Delcourt C, Shan J, Li Q, Xu J . Is Regular Screening for Intracranial Aneurysm Necessary in Patients with Autosomal Dominant Polycystic Kidney Disease? A Systematic Review and Meta-analysis. Cerebrovasc Dis. 2017; 44(1-2):75-82. DOI: 10.1159/000476073. View