Dysplasia Epiphysealis Hemimelica of the Radial Head: a Rare Case Report

Overview

Journal BMC Musculoskelet Disord

Publisher Biomed Central

Specialties Orthopedics
Physiology

Date 2021 Feb 6

PMID 33546632

Authors

Hiva Mohamadian

Mansour Bahardoust

Borzouyeh Molazem Sanandaji

Saba Saberi

Affiliations

Soon will be listed here.

Abstract

Background: Dysplasia epiphysealis hemimelica (DEH) is a rare benign overgrowth generally affecting the epiphyses and short bones of the lower limbs. DEH in the elbow joint is extremely rare, and to date, only three cases of DEH have been reported in the radial head.

Case Presentation: In this study, we report a case of DEH located in the radial head of the right elbow of a 10-year-old boy, which was presented with elbow pain and limited range of motion. In clinical examination, an asymmetrical enlargement was observed over the elbow. The lesion was resected surgically, and the patient's symptoms resolved afterward. The histologic analysis of the lesion confirmed the diagnosis of DEH.

Conclusion: This report highlights the role of DEH in the differential diagnosis of elbow pathologies, particularly its differentiation from osteochondroma.

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