Frontal Fibrosing Alopecia: a Disease That Remains Enigmatic

Overview

Journal Postepy Dermatol Alergol

Publisher Termedia

Specialty Allergy & Immunology

Date 2020 Sep 30

PMID 32994767

Citations 9

Authors

Anna Lis-Swiety

Ligia Brzezinska-Wcislo

Affiliations

Soon will be listed here.

Abstract

Frontal fibrosing alopecia (FFA) is recognized to represent a generalized process of inflammatory scarring alopecia. Apart from the classic form affecting the frontal hairline, there are a range of disease manifestations involving loss of eyebrows and of eyelashes, loss of peripheral body hair, fibrosing alopecia in a pattern distribution, facial and extrafacial skin, mucous membrane, and nail involvement. Classic linear, diffuse "zigzag", pseudo "fringe sign", androgenetic alopecia-like, cockade-like, ophiasis-like and incomplete patterns are distinguished. The aetiology of FFA remains obscure, but a number of pathogenetic hypotheses and treatments to halt disease progression have been proposed.

Citing Articles

Pruritus in Lichen Planopilaris and Frontal Fibrosing Alopecia-Clinical Characteristics and Dermoscopic Correlations.

Kolcz K, Krawczyk-Woloszyn K, Reich A, Zychowska M J Clin Med. 2024; 13(16).

PMID: 39201040 PMC: 11355708. DOI: 10.3390/jcm13164898.

Trichoscopy of Androgenetic Alopecia: A Systematic Review.

Kuczara A, Waskiel-Burnat A, Rakowska A, Olszewska M, Rudnicka L J Clin Med. 2024; 13(7).

PMID: 38610726 PMC: 11012765. DOI: 10.3390/jcm13071962.

Frontal Fibrosing Alopecia and Reproductive Health: Assessing the Role of Sex Hormones in Disease Development.

Roman A, Petca R, Dumitrascu M, Petca A, Ionescu Miron A, Sandru F J Pers Med. 2024; 14(1).

PMID: 38248773 PMC: 10817300. DOI: 10.3390/jpm14010072.

Janus kinase inhibition for the treatment of refractory frontal fibrosing alopecia: A case series and review of the literature.

Dunn C, Griffith V, Coican A, Dane A, Chow W, Aneja S JAAD Case Rep. 2023; 40:47-52.

PMID: 37701887 PMC: 10493233. DOI: 10.1016/j.jdcr.2023.07.037.

Frontal fibrosing alopecia coexisting with vitiligo: is there a true association?.

Pauli Damke J, Ossanai Schoenardie B, Figini Maciel R, Peruzzo J An Bras Dermatol. 2023; 98(6):853-855.

PMID: 37479631 PMC: 10589473. DOI: 10.1016/j.abd.2021.10.018.

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