Congenital Short Bowel Syndrome: a Rare Cause of Neonatal Intestinal Obstruction

Overview

Journal J Int Med Res

Publisher Sage Publications

Specialty General Medicine

Date 2020 Sep 21

PMID 32951488

Citations 1

Authors

Mostafa Zain

Mansour Abdelkader

Ahmed Azab

Mostafa Kotb

Affiliations

Soon will be listed here.

Abstract

Congenital short bowel syndrome (CSBS) is an uncommon gastrointestinal disorder in which an unclear aetiology causes considerable intrauterine reduction in small bowel length. As a result of reduced absorptive intestinal length, chronic diarrhoea, vomiting, and consequently, failure to thrive are likely. We report a case of CSBS in a 26-day-old girl who had malrotation and a short bowel with a length of bowel from the pylorus to the ileocecal junction of approximately 40 cm. The patient underwent Ladd's procedure, but she is still dependent on parenteral nutrition.

Citing Articles

Congenital Short Bowel Syndrome With Annular Pancreas Presenting as Neonatal Intestinal Obstruction.

Naik D, Mahalik S, Pati A Cureus. 2022; 14(11):e31802.

PMID: 36579202 PMC: 9788789. DOI: 10.7759/cureus.31802.

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