Prune Belly Syndrome: Current Perspectives

Overview

Journal Pediatric Health Med Ther

Publisher Dove Medical Press

Date 2019 Sep 10

PMID 31496864

Citations 8

Authors

Angela M Arlen

Cayce Nawaf

Andrew J Kirsch

Affiliations

Soon will be listed here.

Abstract

Prune belly syndrome (PBS) is a rare but morbid congenital disease, classically defined by a triad of cardinal features that includes cryptorchidism, urinary tract dilation and laxity of the abdominal wall musculature. Children often require numerous surgical interventions including bilateral orchidopexy as well as individually tailored urinary tract and abdominal wall reconstruction. Along with the classic features, patients with PBS often experience gastrointestinal, orthopedic, and cardiopulmonary comorbidities.

Citing Articles

Combined Double-breasted Full-thickness Abdominal Flap Plication and Acellular Dermal Matrix in Prune-belly Syndrome Reconstruction.

Baccarani A, Pappalardo M, Ceccarelli P, Starnoni M, De Santis G Plast Reconstr Surg Glob Open. 2024; 12(4):e5744.

PMID: 38645635 PMC: 11029998. DOI: 10.1097/GOX.0000000000005744.

Simultaneous second-stage Fowler-Stephens Orchiopexy and microvascular testicular autotransplantation in a patient with prune belly syndrome with cryptorchidism.

Larson B, Francis A, McMahon D, Massanyi E, Murthy A J Surg Case Rep. 2023; 2023(10):rjad588.

PMID: 37901606 PMC: 10602715. DOI: 10.1093/jscr/rjad588.

A case of prune belly syndrome: Experience from a regional hospital in Togo.

Essobiyou T, Kebalo S, Pali E, Keheou A, Issa M, Dosseh E Int J Surg Case Rep. 2022; 102:107812.

PMID: 36502656 PMC: 9763359. DOI: 10.1016/j.ijscr.2022.107812.

Dental treatment of patients with prune belly syndrome.

Quilici G, Tolarova M, Quilici M, Quilici D Spec Care Dentist. 2022; 43(1):67-72.

PMID: 35526214 PMC: 10083899. DOI: 10.1111/scd.12728.

Surgical Management of a Volvulus of a Wandering Spleen Associated with a Volvulus of the Small Intestine.

Maienza E, Chereau N, Menegaux F Case Rep Surg. 2022; 2022:8696492.

PMID: 35492869 PMC: 9054486. DOI: 10.1155/2022/8696492.

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