Orbital Vasculitides-Differential Diagnosis

Overview

Journal Curr Rheumatol Rep

Publisher Current Science

Specialty Rheumatology

Date 2019 Sep 6

PMID 31486966

Citations 2

Authors

Gabriela M Espinoza

Jessica L Liu

Affiliations

Soon will be listed here.

Abstract

Purpose Of Review: The orbit is subject to a variety of vascular insults that manifest with both specific and nonspecific patterns of vision compromise. The aim of the following review is to highlight the ophthalmic clinical features of systemic vasculitides that most frequently involve the orbit and differentiate them from the most common non-vasculitic orbital disorders.

Recent Findings: New studies continue to explore the autoimmune nature of vasculitic disease and seek to determine optimal use of newer therapies such as biologic agents. The pattern of ocular involvement in the context of clinical history allows the knowledgeable physician to distill a differential diagnosis into a specific or likely cause. Establishing a diagnosis in a timely fashion allows for a custom-tailored approach to therapy.

Citing Articles

Rare Diseases of the Orbit.

Kisser U, Heichel J, Glien A Laryngorhinootologie. 2021; 100(S 01):S1-S79.

PMID: 34352903 PMC: 8365778. DOI: 10.1055/a-1384-4641.

Risk factors of avascular necrosis in Takayasu arteritis: a cross sectional study.

Gokcen N, Komac A, Tuncer F, Kocak Buyuksutcu G, Ozdemir Isik O, Yazici A Rheumatol Int. 2021; 42(3):529-534.

PMID: 34091705 DOI: 10.1007/s00296-021-04909-0.

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