Coexistence of Familial Mediterranean Fever and Behçet's Disease: a Case Report

Overview

Journal Turk J Phys Med Rehabil

Specialty Rehabilitation Medicine

Date 2019 Aug 28

PMID 31453447

Citations 3

Authors

Tuba Guler

Yesim Garip

Fulya Dortbas

Ayse Aslihan Karci

Nursad Cifci

Affiliations

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Abstract

Behçet's disease (BD) is a chronic, multi-systemic vasculitis, characterized by a triad of recurrent aphthous stomatitis, genital aphthae, and uveitis. It is common in the Eastern Mediterranean, Middle East, and Eastern Asian countries. Familial Mediterranean fever (FMF) is an autosomal recessive autoinflammatory disorder, which is common seen in the Turkish, Armenian, Arabic, and Sephardic Jewish populations. It is characterized by recurrent episodes of fever, peritonitis, pleuritis, arthritis, and erysipelas-like skin lesions. Behçet's disease and FMF have common clinical features and geographic distribution. Herein, we present a 19-year-old female patient with coexistence of FMF and BD in the light of literature data.

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Concurrence of familial Mediterranean fever and Behçet's disease: a case report and review of the literature.

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