Blood Film Says It All! Rare Case of Congenital TTP Misdiagnosed As ITP

Overview

Journal Int J Pediatr Adolesc Med

Date 2019 Aug 8

PMID 31388548

Citations 2

Authors

Ayesha Majeed Memon

Natasha Ali

Affiliations

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Abstract

We report a case of a 16-year-old female who presented with bleeding diathesis. Peripheral blood film examination was consistent with microangiopathic hemolytic anemia with 7% fragmented red blood cells. The ADAMTS13 level was 40 ng/ml (reference range: 630-850 ng/ml). She responded to plasma exchange therapy and methylprednisolone and was discharged in a stable condition.

Citing Articles

Hereditary thrombotic thrombocytopenic purpura mimicking immune thrombocytopenia was revealed by miscarriage-novel compound heterozygous mutations in hTTP.

Zhou R, Wang J, Wang A, Wang S, Li Y, Xu S BMC Med Genomics. 2024; 17(1):281.

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Thrombotic Thrombocytopenic Purpura: Revisiting a Miss and an Inevitable Consequence.

Gogia P, Gbujie E, Benge E, Bhasin S Cureus. 2020; 12(7):e9283.

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