Precision Surgery for Pheochromocytomas and Paragangliomas

Overview

Journal Horm Metab Res

Specialty Endocrinology

Date 2019 Jul 16

PMID 31307109

Citations 4

Authors

Douglas Wiseman

Mustapha El Lakis

Naris Nilubol

Affiliations

Soon will be listed here.

Abstract

Since Felix Fränkel's account of pheochromocytoma in 1886, great discoveries and vast advancements in the diagnosis, genetics, anatomical and functional imaging techniques, and surgical management of pheochromcytoma and paraganglioma (P-PGL) have been made. The improved insight in the pathophysiology of P-PGL and more accurate detection methods enable physicians to tailor the treatment plan to an individual based on the genetic profile and tumor behavior. This review will cover briefly the clinical features, diagnosis, genetic mutations, and imaging modalities that are used to guide current surgical management of these rare and interesting endocrinopathies.

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Progress in surgical approaches and outcomes of patients with pheochromocytoma and paraganglioma.

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exon 1 deletion: A recurrent germline mutation in Colombian patients with pheochromocytomas and paragangliomas.

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