Fever with Persistent Flagellate Erythema in a Primigravida: a Rare Presentation of Adult-onset Still's Disease

Overview

Journal BMJ Case Rep

Specialty General Medicine

Date 2019 Jul 15

PMID 31302619

Citations 2

Authors

Riti Bhatia

Nidhi Kaeley

Ravi Kant

Ankith Basi

Affiliations

Soon will be listed here.

Abstract

We describe a case of a 25-year-old primigravida, who presented to the emergency department with fever, arthralgia and erythematous maculopapular eruption. There was confluent violaceous macular erythema on the arms, v-area of the neck and upper back with periorbital oedema, mimicking dermatomyositis. There was flagellate erythema on the back. Skin biopsy and systemic investigations helped to rule out dermatomyositis. A final diagnosis of adult-onset Still's disease with atypical cutaneous manifestations was made. This atypical variant is associated with a worse prognosis. Early recognition of this clinical variant can be life-saving for the patient.

Citing Articles

Adult-Onset Still's Disease with Distinctive Skin Signs and Elevated LDH.

Klimi E, Kataxaki E Mediterr J Rheumatol. 2024; 35(2):316-318.

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Persistent Pruritic Linear Streaks of Adult-Onset Still's Disease: Reconsidering the Yamaguchi Criteria.

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