Opinion for Different Centers: Surgical Experience with Chiari Malformation Type I in Children at Xuanwu Hospital, China

Overview

Journal Childs Nerv Syst

Specialty Pediatrics

Date 2019 Jun 20

PMID 31214817

Authors

Kai Wang

Hao Wu

Jian Fengzeng

Gao Zeng

Affiliations

Soon will be listed here.

Abstract

Purpose: To evaluate the presenting symptoms, surgical strategy, and outcome in children with Chiari malformation type I (CM-I).

Methods: The medical records of children who were diagnosed with CM-I under 14 years old and subsequently underwent surgery for CM-I between 2014 and 2018 were reviewed. The medical records for presentation, radiological image, surgical intervention, and outcome were evaluated.

Results: Twelve children with CM-I and syringomyelia were included. All of the children were symptomatic. The most common presenting symptom was weakness, followed by scoliosis. All of them underwent posterior fossa decompression with/without duraplasty. Relief of preoperative pathologies and syringomyelia was experienced by all of them.

Conclusions: The presenting symptoms of CM-I in children may be neurological deficits and scoliosis, which have a relationship with syringomyelia. Early recognition and a tailored operative procedure of CM-I in children could lead to good outcomes. Additional therapies for syringomyelia and scoliosis could be avoided.

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