Kikuchi-Fujimoto Disease: An Atypical Presentation of a Rare Disease

Overview

Journal Cureus

Specialty Biomedical Engineering

Date 2019 Apr 17

PMID 30989008

Citations 5

Authors

Amanda Moyer

Muhammad Z Hanafi

Teresa Scordino

Michael Bronze

Affiliations

Soon will be listed here.

Abstract

Kikuchi-Fujimoto disease (KFD), or necrotizing histiocytic lymphadenitis, is a rare cause of lymphadenopathy and fever. Although the clinical course is usually benign, KFD is often mistaken for malignancy or infection. Recognition of typical and atypical cases of KFD is necessary to avoid unnecessary interventions. Here we report an atypical presentation of KFD with diffuse lymphadenopathy and leukocytosis associated with high levels of circulating Epstein-Barr viral DNA.

Citing Articles

Kikuchi-Fujimoto Disease: A Rare Cause of Pyrexia of Unknown Origin and Cervical Lymphadenopathy.

Fadul A, Subahi E, Ali E, Awadalkareem H, Mohamed G, Elawad M Cureus. 2022; 14(10):e30823.

PMID: 36451640 PMC: 9703205. DOI: 10.7759/cureus.30823.

Kikuchi-Fujimoto's Disease or Histiocytic Necrotizing Lymphadenitis Following mRNA COVID-19 Vaccination: A Rare Case.

Daghri S, Belmoufid N, Rami A, Al Bouzidi A, Bouanani N Cureus. 2022; 14(4):e24155.

PMID: 35592214 PMC: 9110038. DOI: 10.7759/cureus.24155.

Bilateral preretinal hemorrhage associated with Kikuchi-Fujimoto disease.

Akhavanrezayat A, Cooper J, Hassan M, Pham B, Nguyen Q, Farr A Am J Ophthalmol Case Rep. 2021; 22:101041.

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An atypical presentation of Kikuchi-Fujimoto disease: A case report & literature review.

Halawa A, Ahmad M, Nashwan A Clin Case Rep. 2020; 8(12):3515-3519.

PMID: 33363963 PMC: 7752579. DOI: 10.1002/ccr3.3373.

Evaluation of a unilateral neck mass in a 16-year-old female: Kikuchi-Fujimoto disease with superimposed bacterial lymphadenitis.

Burns J, Pathania S, Griesser R, Norelli J, Gilgeours K, Tugetman J SAGE Open Med Case Rep. 2020; 8:2050313X20962640.

PMID: 33224497 PMC: 7649878. DOI: 10.1177/2050313X20962640.

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