Primary Rosai-Dorfman Disease of Bone: A Report of Two Cases

Overview

Journal Case Rep Radiol

Publisher Wiley

Specialty Radiology

Date 2019 Feb 6

PMID 30719368

Citations 2

Authors

Andrew B Ross

Kirkland W Davis

Darya Buehler

Brian Y Chan

Affiliations

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Abstract

Rosai-Dorfman disease (RDD), sometimes known as sinus histiocytosis with massive lymphadenopathy, is a rare histiocytic disorder that most commonly presents as painless, massive cervical lymphadenopathy in young adults. Extranodal disease can occur in up to 40% of patients but primary involvement of bone is rare. We present two cases of primary RDD of bone: one case of multifocal osseous RDD presenting as a painful lesion in the elbow, and one case of a solitary osseous lesion presenting as a painful lesion in the wrist.

Citing Articles

Primary intraosseous Rosai-Dorfman disease: An analysis of clinicopathologic characteristics, molecular genetics, and prognostic features.

Weng X, Yang Y, Zhang M, Cai C, Sun Y, Wu X Front Oncol. 2022; 12:950114.

PMID: 36185213 PMC: 9520307. DOI: 10.3389/fonc.2022.950114.

Primary Bone Lesions in Rosai-Dorfman Disease, a Rare Case and Diagnostic Challenge-Case Report and Literature Review.

Adam R, Harsovescu T, Tudorache S, Moldovan C, Pogarasteanu M, Dumitru A Diagnostics (Basel). 2022; 12(4).

PMID: 35453831 PMC: 9032234. DOI: 10.3390/diagnostics12040783.

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