The Epidemiology of Deafness

Overview

Journal Cold Spring Harb Perspect Med

Specialty General Medicine

Date 2018 Sep 26

PMID 30249598

Citations 71

Authors

Abraham M Sheffield

Richard J H Smith

Affiliations

Soon will be listed here.

Abstract

Hearing loss is the most common sensory deficit worldwide. It affects ∼5% of the world population, impacts people of all ages, and exacts a significant personal and societal cost. This review presents epidemiological data on hearing loss. We discuss hereditary hearing loss, complex hearing loss with genetic and environmental factors, and hearing loss that is more clearly related to environment. We also discuss the disparity in hearing loss across the world, with more economically developed countries having overall lower rates of hearing loss compared with developing countries, and the opportunity to improve diagnosis, prevention, and treatment of this disorder.

Citing Articles

A KCNQ4 Gene Variant (c.701A > G; p.His234Arg) in a Chinese Family With Nonsyndromic Deafness 2A.

Gong G, Huang C, Jin H, Zhang Z, Yang C, Yang G Mol Genet Genomic Med. 2025; 13(3):e70075.

PMID: 40052770 PMC: 11886983. DOI: 10.1002/mgg3.70075.

Prevalence and Clinical Characteristics of -Associated Hearing Loss Identified in a Cohort of 7065 Japanese Patients with Hearing Loss.

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Garcia A, Arabi A, Croteau C, de Lacerda A PLoS One. 2025; 20(2):e0308592.

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The Prevalence and Clinical Characteristics of -Associated Hearing Loss in 15,684 Hearing Loss Patients.

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