Congenital Pulmonary Airway Malformation

Overview

Journal Autops Case Rep

Date 2018 May 22

PMID 29780758

Citations 5

Authors

Wlamir Pestana Ursini

Cesar Cilento Ponce

Affiliations

Soon will be listed here.

Abstract

Congenital pulmonary airway malformation (CPAM) is a developmental malformation of the lower respiratory tract. We report the case of a male newborn diagnosed with cystic lung disease during prenatal ultrasound. A cesarean section was performed at the 32nd gestational week because of premature rupture of the membranes, and soon after the delivery the newborn developed respiratory failure and died. The aim of this study is to report an autopsy case because of its rarity, and to briefly discuss the CPAM subtypes and differential diagnosis of cystic lung diseases of childhood.

Citing Articles

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