Hemorrhagic Bullous Lesions in Henoch-Schönlein Purpura: a Case Report and Review of the Literature

Overview

Journal BMC Pediatr

Publisher Biomed Central

Specialty Pediatrics

Date 2018 May 12

PMID 29747613

Citations 4

Authors

Hung-Wen Su

Chiu-Yu Chen

Yee-Hsuan Chiou

Affiliations

Soon will be listed here.

Abstract

Background: Henoch-Schönlein purpura (HSP) is a common vasculitis in childhood characterized by purpura, arthritis, abdominal pain and renal involvement. However, bullous HSP is a rare cutaneous manifestation, and a few cases have been reported.

Case Presentation: Herein, we report a 15-year-old male with bullous HSP who presented with severe abdominal pain and hemorrhagic bullous lesions over his lower extremities. He was treated with corticosteroid, after which the symptoms improved dramatically. No recurrence was noted after follow-up, though scarring was present. We also reviewed the literature related to bullous HSP and identified 39 cases, most of whom were treated with corticosteroids.

Conclusion: Clinicians should be aware of the atypical types of HSP, including bullous HSP. Most patients with bullous HSP have a good prognosis.

Citing Articles

Bullous Henoch-Schönlein Purpura and Associated Nephritis: A Pathological Case Report.

Popov H, Koleva T, Stoyanov G Cureus. 2023; 15(2):e35051.

PMID: 36942172 PMC: 10024341. DOI: 10.7759/cureus.35051.

Systemic disease in leukocytoclastic vasculitis: a focus on direct immunofluorescence findings.

Ertekin S, Aksu A, Leblebici C, Erdemir V, Erdem O, Avci E An Bras Dermatol. 2022; 98(1):59-67.

PMID: 36369199 PMC: 9837647. DOI: 10.1016/j.abd.2021.11.009.

Recurrent Henoch-Schönlein Purpura with bullous rash and pulmonary nodules.

Zheng C, Childers J, Rabinovich E, Nazareth-Pidgeon K Pediatr Rheumatol Online J. 2020; 18(1):40.

PMID: 32448396 PMC: 7245848. DOI: 10.1186/s12969-020-00436-7.

Hemorrhagic Bullous Henoch-Schönlein Purpura: Case Report and Review of the Literature.

Nothhaft M, Klepper J, Kneitz H, Meyer T, Hamm H, Morbach H Front Pediatr. 2019; 6:413.

PMID: 30723709 PMC: 6349767. DOI: 10.3389/fped.2018.00413.

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