Congenital Absence of the Right Coronary Artery: A Case Report and Literature Review

Overview

Journal Medicine (Baltimore)

Specialty General Medicine

Date 2018 Mar 22

PMID 29561437

Citations 11

Authors

Gao-Wu Yan

Anup Bhetuwal

Guo-Qing Yang

Quan-Shui Fu

Na Hu

Lin-Wei Zhao

Hong Chen

Xiao-Ping Fan

Jing Yan

Hao Zeng

Qing Zhou

Affiliations

Soon will be listed here.

Abstract

Rationale: Congenital absence of the right coronary artery (RCA) is a rare congenital malformation of the cardiovascular system which may have fatal consequences.

Patient Concerns: A 63-year-old man with a 5-year history of chest pain after exertion which had aggravated for >1 month was advised for admission and computed tomography angiography (CTA) examination of the coronary artery to screen for coronary artery disease (CAD).

Diagnoses: The coronary artery CTA showed absence of RCA arising form the aortic root after which a selective coronary angiography (SCA) examination was done that confirmed the diagnosis of congenital absence of RCA.

Interventions: As the patient refused to receive a coronary artery stent implantation citing his financial condition, only symptomatic treatment was given.

Outcomes: The patient requested to be discharged from the hospital against the advice of his doctors 1 week later. A query made by the telephone suggested that the patient's symptoms were under control by use of prescribed medications only.

Lessons: Although being a rare condition, a coronary artery CTA examination can be utilized to screen for congenital absence of RCA and other varieties of cardiovascular malformation whereas SCA can be performed to confirm the diagnosis.

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