Successful Surgical Repair and Perioperative Management of 6-Month-Old With Total Anomalous Pulmonary Venous Return in a Developing Country: Considerations for the Treatment of Pulmonary Hypertension

Overview

Journal Cardiol Res

Specialty Cardiology & Vascular Diseases

Date 2018 Feb 27

PMID 29479388

Citations 1

Authors

Lakshmi R Gokanapudy

Kenneth E Remy

Sathappan Karuppiah

Eneida V Melgar Humala

Ibrahim Abdullah

Michael D Ruppe

William S Schechter

Robert Michler

Joseph D Tobias

Affiliations

Soon will be listed here.

Abstract

Total anomalous pulmonary venous return (TAPVR) is a rare congenital cardiac defect, accounting for 1.5-3% of cases of congenital heart disease. With prenatal ultrasonography, the majority of these patients are diagnosed in utero with definitive surgery performed during the neonatal period. However, as prenatal screening may not be available in developing countries, patients may present in later infancy. We present successful surgical repair of a 6-month-old infant with TAPVR who presented for medical care at 5 months of age in Lima, Peru. The late presentation of such infants and the limited resources available for the treatment of elevated pulmonary vascular resistance may impact successful surgical correction of such defects. The perioperative care of such infants in developing countries is discussed and strategies for managing postoperative pulmonary hypertension is reviewed.

Citing Articles

Total Anomalous Pulmonary Venous Return in the Time of SARS-CoV-2-Case Report.

Luca A, Curpan A, Manea R, Butnariu L, Tarca E, Starcea I Children (Basel). 2023; 10(2).

PMID: 36832516 PMC: 9955405. DOI: 10.3390/children10020387.

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