Adult-onset Adrenoleukodystrophy Presenting As a Psychiatric Disorder: MRI Findings

Overview

Journal Dement Neuropsychol

Date 2017 Dec 8

PMID 29213811

Citations 3

Authors

Antonio Cezar Ribeiro Galvao

Gislaine Cristina Lopes Machado-Porto

Fabio Henrique de Gobbi Porto

Leandro Tavares Lucato

Ricardo Nitrini

Affiliations

Soon will be listed here.

Abstract

A 35-year-old, previously healthy man presented psychiatric symptoms lasting four years, receiving treatment with neuroleptics. One year later he evolved with gait disequilibrium. After a further six months, cognitive symptoms were characterized with rapid evolution to a profound demented state. MRI showed signal changes in cerebral white matter and very long-chain fatty acids were detected in blood.

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