Harlequin Syndrome and Horner Syndrome After Neck Schwannoma Excision in a Pediatric Patient: A Case Report

Overview

Journal Medicine (Baltimore)

Specialty General Medicine

Date 2017 Nov 16

PMID 29137067

Citations 4

Authors

Dong Hoon Lee

Jong Yuap Seong

Tae Mi Yoon

Joon Kyoo Lee

Sang Chul Lim

Affiliations

Soon will be listed here.

Abstract

Rationale: Harlequin syndrome is an extremely rare benign condition characterized by unilateral facial flushing and sweating.

Patient Concern: An 11-year-old boy presented with complaint of a right neck mass of 1-month duration.

Diagnosis: The preoperative diagnosis was neurogenic tumor of vagus nerve or sympathetic nerve.

Interventions: We performed right neck mass removal under general anesthesia.

Outcomes: We report a case of harlequin syndrome associated with Horner syndrome in an 11-year boy who underwent excision of right neck schwannoma.

Lessons: Clinicians should consider the point that harlequin syndrome could occur as a first sign of more serious conditions.

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Harlequin Syndrome after Thoracoscopic Repair of a Child with Tracheoesophageal Fistula (TEF).

Wagner R, Lacher M, Merkenschlager A, Markel M European J Pediatr Surg Rep. 2019; 7(1):e63-e65.

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