Ectopic Cerebellar Tissue in the Occipital Bone: a Case Report

Overview

Journal J Med Case Rep

Publisher Biomed Central

Specialty General Medicine

Date 2017 Aug 22

PMID 28823247

Citations 2

Authors

Mariko Kawashima

Masahito Kobayashi

Keisuke Ishizawa

Takamitsu Fujimaki

Affiliations

Soon will be listed here.

Abstract

Background: Ectopic cerebellar tissue located distantly from the normal cerebellum is very rare, and its pathophysiology remains to be elucidated.

Case Presentation: We report an extremely rare case of intraosseous ectopic cerebellum detected incidentally at suboccipital craniotomy in a 46-year-old Japanese woman with hemifacial spasm. She had a small bone defect in the occipital bone, which contained a tiny area of soft tissue surrounded by cerebrospinal fluid connecting to the normal subarachnoid space through a dural opening. Histopathology demonstrated cerebellar cortex tissue consisting of molecular and granular cell layers.

Conclusions: This is the first report of glioneuronal ectopia within the skull bone separated from normal brain tissue, and it is important to distinguish this entity from other osteolytic lesions.

Citing Articles

Neuroimaging Features of Ectopic Cerebellar Tissue: A Case Series Study of a Rare Entity.

Orman G, Kralik S, Battini R, Buchignani B, Desai N, Goetti R AJNR Am J Neuroradiol. 2021; 42(6):1167-1173.

PMID: 34255731 PMC: 8191659. DOI: 10.3174/ajnr.A7105.

Ectopic Cerebellar Tissue in the Occipital Bone: A Case Report.

Gupta M, Duddleston P, Sagi V, Powers M, U H J Neurol Surg Rep. 2020; 81(3):e42-e45.

PMID: 32782896 PMC: 7414970. DOI: 10.1055/s-0040-1712917.

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