Hirschsprung Disease - Current Diagnosis and Management

Overview

Journal Indian J Pediatr

Specialty Pediatrics

Date 2017 Jun 11

PMID 28600660

Citations 27

Authors

Kanishka Das

Suravi Mohanty

Affiliations

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Abstract

Hirschsprung disease is a common cause of neonatal and infantile large gut obstruction. It is characterised by varying extent of contiguous aganglionosis extending from the anorectum proximally. Since its recognition, the diagnosis and management has continuously evolved with advances in histological evaluation and surgical techniques. This article summarizes the current modalities of investigation and optimal surgical management of Hirschsprung disease and concludes with a reference to the Indian scenario.

Citing Articles

Therapeutic approaches in Hirschsprung's disease: clinical cases.

tandea V, Raducan I, Neagu O, Constantinoiu S J Med Life. 2024; 17(6):644-648.

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Ultrasound imaging of bowel obstruction in neonates.

Salman R, Mertiri L, Seghers V, Schiess D, Nguyen H, Sher A J Ultrasound. 2024; 27(2):407-417.

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Postoperative Hirschsprung's associated enterocolitis (HAEC): transition zone as putative histopathological predictive factor.

Duci M, Santoro L, Dei Tos A, Loss G, Mescoli C, Gamba P J Clin Pathol. 2023; 78(2):111-116.

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Enhancing diagnosis of Hirschsprung's disease using deep learning from histological sections of post pull-through specimens: preliminary results.

Duci M, Magoni A, Santoro L, Dei Tos A, Gamba P, Uccheddu F Pediatr Surg Int. 2023; 40(1):12.

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Associated congenital heart disease with Hirschsprung's disease: a retrospective cohort study on 2,174 children.

Wu Y, Zhu Y, Zhang X, Feng J, Xia H, Zhang Y Front Cardiovasc Med. 2023; 10:1215473.

PMID: 37636298 PMC: 10450952. DOI: 10.3389/fcvm.2023.1215473.

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