Congenital Vomer Agenesis: Report of Two Cases

Overview

Journal Iran J Otorhinolaryngol

Publisher Mashhad University of Medical Sciences

Specialty Otorhinolaryngology

Date 2017 Jun 8

PMID 28589112

Authors

Mehdi Bakhshaee

Sherwin Tavakol

Yeganeh Teimouri

Affiliations

Soon will be listed here.

Abstract

Introduction: Congenital vomer agenesis is an extremely rare condition in which the vomer bone does not fully develop, which can lead to septal perforation.

Case Report: We report two cases with a defect in the vomer bone in the posteroinferior portion of the septum, found accidentally while performing a pre-operative CT scan for nasal obstruction evaluation. They were diagnosed with congenital vomer agenesis.

Conclusion: There are afew reports of vomer agenesis in literatures. By increasing usage of sinonasal endoscopic examination,we expect to address more cases in the future.

References

Sakizlioglu I, Frommer J, SHIERE F . Prenatal development of the vomer in normal and cleft palate mice. Am J Anat. 1974; 141(3):433-9. DOI: 10.1002/aja.1001410312. View

Dogru H, Yasan H, Tuz M . Congenital vomeral bone defect in two thalassemia trait cases. Eur Arch Otorhinolaryngol. 2003; 261(3):136-8. DOI: 10.1007/s00405-003-0619-6. View

Mohri M, AMATSU M . Congenital defects of the vomer. Ann Otol Rhinol Laryngol. 2000; 109(5):497-9. DOI: 10.1177/000348940010900510. View

Hansen L, Nolting D, Holm G, Hansen B, Kjaer I . Abnormal vomer development in human fetuses with isolated cleft palate. Cleft Palate Craniofac J. 2004; 41(5):470-3. DOI: 10.1597/03-058.1. View

Lee J . Congenital vomeral bone defect: report of two cases and a review of the literature. Acta Otolaryngol. 2006; 126(11):1229-31. DOI: 10.1080/00016480500504218. View

Yorgancilar E, Yildirim M, Gun R, Meric F, Topcu I . Congenital os vomer agenesis: case report and literature review. Ear Nose Throat J. 2012; 91(4):164-71. DOI: 10.1177/014556131209100408. View

Kjaer I . Human prenatal palatal closure related to skeletal maturity of the jaws. J Craniofac Genet Dev Biol. 1989; 9(3):265-70. View

Sandikcioglu M, Molsted K, Kjaer I . The prenatal development of the human nasal and vomeral bones. J Craniofac Genet Dev Biol. 1994; 14(2):124-34. View

Calvo D, Cuetos Azcona M, Vallejo Valdezate L, Gil-Carcedo Garcia L . [Agenesis of the vomer bone]. Acta Otorrinolaringol Esp. 2008; 59(3):148-9. View

10.

Yilmaz M, Altuntas A . Congenital vomeral bone defect. Am J Otolaryngol. 2005; 26(1):64-6. DOI: 10.1016/j.amjoto.2004.06.016. View

11.

Verim A, Calim O, Yenigun A, Kocagoz G, Kokten N, Ozkul H . Hereditary characteristic of isolated congenital vomer aplasia. J Craniomaxillofac Surg. 2012; 40(8):e392-6. DOI: 10.1016/j.jcms.2012.02.009. View

12.

Ucar S, Aydin O, Ozturk M . [Congenital vomer agenesis]. Kulak Burun Bogaz Ihtis Derg. 2015; 25(3):182-4. DOI: 10.5606/kbbihtisas.2015.37108. View