A Case of Multiple Unilateral Pulmonary Arteriovenous Malformation Relapse: Efficacy of Embolization Treatment

Overview

Journal Open Med (Wars)

Specialty General Medicine

Date 2017 Mar 30

PMID 28352746

Citations 1

Authors

Rossella Masiello

Carlo Iadevaia

Edoardo Grella

Carmelindo Tranfa

Francesco Cerqua

Giovanni Rossi

Giuseppe Santoro

Bruno Amato

Aldo Rocca

Roberta DE Dona

Sabrina Lavoretano

Fabio Perrotta

Affiliations

Soon will be listed here.

Abstract

Pulmonary arteriovenous Malformations (PAVMs) are a rare vascular alteration characterized by abnormal communications between the pulmonary arteries and veins resulting in an extracardiac right-to-left (R-L) shunt. The majority of PAVMs are associated with an autosomal dominant vascular disorder also known as Osler-Weber-Rendu Syndrome. PAVMs appearance can be both single and multiple. Clinical manifestations include hypoxemia, dyspnea cyanosis, hemoptysis and cerebrovascular ischemic events or abscesses. We report a case of an 18 year old female with severe respiratory failure caused by a relapse of multiple unilateral pulmonary arterovenous fistula. Symptoms at admission include dyspnea, cyanosis and clubbing. The patient underwent pulmonary angio-TC scan, brain CT and echocardiography. The thoracic angio-CT scan showed the presence of PAVMs of RUL and RLL; a marked increase of right bronchial artery caliber and its branches with an aneurismatic dilatation was also observed. The patient underwent percutaneous transcatheter embolization using Amplatzer Vascular Plug IV; a relevant clinical and functional improvement was subsequently recorded. Embolization is effective in the treatment of relapsing PAVMS.

Citing Articles

Analysis of 18 complex diffuse arteriovenous malformation cases treated with percutaneous radiofrequency ablation.

Ge C, Tai M, Chen T, Li K, Xu Z, Qin Z BMC Cardiovasc Disord. 2021; 21(1):373.

PMID: 34344307 PMC: 8335943. DOI: 10.1186/s12872-021-02169-1.

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