Cardiac Involvement Classification and Therapeutic Management in Patients with Duchenne Muscular Dystrophy

Overview

Journal J Neuromuscul Dis

Publisher Sage Publications

Specialty Neurology

Date 2017 Mar 9

PMID 28269790

Citations 28

Authors

Abdallah Fayssoil

Soumeth Abasse

Katy Silverston

Affiliations

Soon will be listed here.

Abstract

Duchenne muscular dystrophy (DMD) is an inherited myogenic disorder due to mutations in the dystrophin gene on chromosome Xp21.1. The clinical picture included peripheral muscle weakness, cardiomyopathy and chronic respiratory insufficiency. In this paper, the authors review cardiac involvement in patients with DMD, propose a cardiac impairment classification and discuss therapeutic management options.

Citing Articles

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