A Case of Proteinase 3 Anti-neutrophil Cytoplasmic Antibody (PR3-ANCA) Positive/IgG4-related Lung Disease

Overview

Journal Respir Med Case Rep

Date 2017 Jan 26

PMID 28119817

Citations 2

Authors

Hirokazu Touge

Katsuyuki Tomita

Akira Yamasaki

Eiji Shimizu

Affiliations

Soon will be listed here.

Abstract

IgG4-related lung disease (IgG4-RLD) is a rare and chronic progressive autoimmune disease. We report a case of IgG4-related inflammatory pseudo-tumor of the lung that was seropositive for proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA). A 61-year-old male had a mass lesion in the right lower lung field in chest X-ray. Transbronchial lung biopsy resulted in a pathological diagnosis of IgG4-RLD. The condition was improved by hormonal therapy.

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