Extracorporeal Membrane Oxygenation Rescue in Adolescent with Bronchiolitis Obliterans-organizing Pneumonia Like Wegener's Granulomatosis
Overview
Authors
Affiliations
We report a 17-year-old woman with bronchiolitis obliterans-organizing pneumonia (BOOP)-like granulomatosis with polyangiitis developing severe airway obliterations. Pending age, phase and grade of autoimmune treatment, and offering ECMO treatment may be crucial for survival but occasionally preface futility. ECMO-treated patient with BOOP-like GPA has never been described before.
Luca S, Pagliuca F, Perrotta F, Ronchi A, Mariniello D, Natale G Int J Mol Sci. 2024; 25(7).
PMID: 38612431 PMC: 11011777. DOI: 10.3390/ijms25073618.
The use of ECMO in pediatric granulomatosis with polyangiitis.
Finkel R, Honig J, Chao C, Rescoe E, Solomon S Pediatr Rheumatol Online J. 2022; 20(1):35.
PMID: 35538584 PMC: 9092879. DOI: 10.1186/s12969-022-00693-8.
ECMO Rescues Patients With Acute Respiratory Failure Related to GPA.
Wan R, Yang W, Ma X, Yang W, Pan P, Hu C Front Med (Lausanne). 2021; 8:671396.
PMID: 34124098 PMC: 8192709. DOI: 10.3389/fmed.2021.671396.