Neuro-Sweet Disease Causing Orbital Inflammation

Overview

Journal Neuroophthalmology

Specialty Neurology

Date 2016 Dec 9

PMID 27928331

Citations 1

Authors

Parisa Taravati

Affiliations

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Abstract

Neuro-Sweet disease is a rare condition causing encephalitis or meningitis in addition to the erythematous skin plaques of Sweet syndrome. Neuro-Sweet disease has been associated with several ocular manifestations, including ocular movement disorders, episcleritis, conjunctivitis, uveitis, and optic disc oedema. The author reports a patient with orbital inflammation, cranial neuropathies, and a skin rash in the setting of myelodysplastic syndrome. Biopsy of her skin lesion confirmed the diagnosis of neuro-Sweet disease. To the author's knowledge, this is the first reported case of neuro-Sweet disease causing orbital inflammation. Her ocular inflammation resolved with the use of systemic corticosteroid treatment.

Citing Articles

Protean Neurologic Manifestations of Two Rare Dermatologic Disorders: Sweet Disease and Localized Craniofacial Scleroderma.

Wallach A, Magro C, Franks Jr A, Shapiro L, Kister I Curr Neurol Neurosci Rep. 2019; 19(3):11.

PMID: 30747288 DOI: 10.1007/s11910-019-0929-8.

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