Young Patient with Generalized Lymphangiomatosis: Differentiating the Differential

Overview

Journal Indian J Radiol Imaging

Publisher Thieme

Specialty Radiology

Date 2016 Nov 19

PMID 27857472

Citations 4

Authors

Tharani Putta

Aparna Irodi

Balamugesh Thangakunam

Ashwin Oliver

Rajesh Gunasingam

Affiliations

Soon will be listed here.

Abstract

We present the case of a 19-year-old man who was extensively evaluated in multiple centres for long-standing cough, dyspnea, and hemoptysis without a definitive diagnosis. His chest radiograph at presentation showed mediastinal widening, bilateral pleural effusions, and Kerley B lines. Computed tomography of the thorax showed a confluent, fluid-density mediastinal lesion enveloping the mediastinal viscera without any mass effect. There were bilateral pleural effusions, prominent peribronchovascular interstitial thickening, interlobular septal thickening and lobular areas of ground glass density with relative sparing of apices. There were a few dilated retroperitoneal lymphatics and well-defined lytic lesions in the bones. In this case report, we aim to systematically discuss the relevant differentials and arrive at a diagnosis. We also briefly discuss the treatment options and prognosis along with our patient's course in the hospital and final outcome.

Citing Articles

Generalized lymphangiomatosis in patients treated for chylothorax following thoracoscopic sympathectomy: Case report.

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Late diagnosis of generalized lymphangiomatosis in a woman presenting with respiratory distress.

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Diffuse pulmonary lymphangiomatosis.

Biscotto I, Rodrigues R, Forny D, Barreto M, Marchiori E J Bras Pneumol. 2019; 45(5):e20180412.

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Gorham's syndrome vs generalized lymphagiomatosis: A close call.

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