Orofacial Manifestations of Systemic Sclerosis

Overview

Journal Br Dent J

Specialty Dentistry

Date 2016 Sep 24

PMID 27659631

Citations 14

Authors

B J Veale

R Y Jablonski

T M Frech

J D Pauling

Affiliations

Soon will be listed here.

Abstract

Systemic sclerosis (SSc) is a multisystem disease of unknown aetiology characterised by microangiopathy, dysregulated immune function and tissue remodelling, which commonly involves the oral cavity. Orofacial manifestations of SSc contribute greatly to overall disease burden and yet are regularly overlooked and under-treated. This may reflect a pre-occupation amongst rheumatology clinicians on potentially life-threatening internal organ involvement, but is also a consequence of insufficient engagement between rheumatologists and dental professionals. A high proportion of SSc patients report difficulty accessing a dentist with knowledge of the disease and there is recognition amongst dentists that this could impact negatively on patient care. This review shall describe the clinical features and burden of orofacial manifestations of SSc and the management of such problems. The case is made for greater collaborative working between rheumatologists and dental professionals with an interest in SSc in both the research and clinical setting.

Citing Articles

Clinician and patient experiences of managing and living with oral and dental manifestations of scleroderma: A scoping review.

Mills T, Price E, Aggarwal V, Del Galdo F, Walker L J Scleroderma Relat Disord. 2024; 9(2):86-98.

PMID: 38910600 PMC: 11188842. DOI: 10.1177/23971983231193515.

Evaluation of oral health in 148 patients with systemic sclerosis-data from a prospective interdisciplinary monocentric cohort.

Pecher A, Gunaydin B, Finke H, Henes J Rheumatol Int. 2024; 44(8):1567-1573.

PMID: 38874787 PMC: 11222211. DOI: 10.1007/s00296-024-05635-z.

Orofacial Complications of the Connective Tissue Disease Systemic Sclerosis.

Sharma M, Fadl A, Leask A J Dent Res. 2024; 103(7):689-696.

PMID: 38779873 PMC: 11191658. DOI: 10.1177/00220345241249408.

Periodontitis Burden in Diffuse Versus Limited Systemic Sclerosis Subtypes: A Pilot Study.

Stanomir A, Micu I, Picos A, Roman A, Soanca A, Onet D Curr Health Sci J. 2023; 49(2):280-287.

PMID: 37779832 PMC: 10541067. DOI: 10.12865/CHSJ.49.02.280.

Orofacial consequences of systemic sclerosis: A systematic review.

Smirani R, Poursac N, Naveau A, Schaeverbeke T, Devillard R, Truchetet M J Scleroderma Relat Disord. 2022; 3(1):81-90.

PMID: 35382129 PMC: 8892883. DOI: 10.1177/2397198317746966.

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