Long Term Follow Up After Resection Emphasizes the Role of Surgery in Primary Hepatic Epithelioid Hemangioendothelioma

Overview

Journal Ann Med Surg (Lond)

Publisher Wolters Kluwer

Specialty Medical Education

Date 2016 Sep 6

PMID 27594996

Citations 13

Authors

Arianeb Mehrabi

Katrin Hoffmann

Karl Heinz Weiss

Carolin Mogler

Peter Schemmer

Markus W Buchler

Ingo Alldinger

Affiliations

Soon will be listed here.

Abstract

Background: Primary Hepatic Epithelioid Hemangioendothelioma is an extremely rare tumor of vascular origin.

Patients: In this work we present clinical data and long term results of eight patients who were surgically treated in our institution. Liver transplantation was performed in five patients (four cadaveric and one living related) and major liver resection in three patients. Three patients are alive with recurrent tumor. After a median follow-up of 100 months (48-266) all patients are alive.

Conclusions: Only surgery can provide cure in HEH. If the extent of the disease prohibits primary resection liver transplantation might offer the most valuable option.

Citing Articles

Long-term prognosis and treatment modalities of hepatic epithelioid hemangioendothelioma: a retrospective study of 228 patients.

Liu X, Yang P, Liu L, Si S, Zhou R, Liu T BMC Cancer. 2024; 24(1):1285.

PMID: 39415114 PMC: 11481724. DOI: 10.1186/s12885-024-13053-4.

Short-term outcomes of combined therapy with sirolimus and interferon-alpha 2b for advanced hepatic epithelioid hemangioendothelioma.

Liu X, Zhou R, Liu L, Si S, Yang S, Han D Ther Adv Med Oncol. 2024; 16:17588359231220509.

PMID: 38188469 PMC: 10768615. DOI: 10.1177/17588359231220509.

CT appearances and classification of hepatic epithelioid hemangioendothelioma.

Tan H, Zhou R, Yu H, Teng F, Si S, Liu L Insights Imaging. 2023; 14(1):56.

PMID: 37005950 PMC: 10067783. DOI: 10.1186/s13244-023-01410-z.

Case report: Successful treatment with the combined therapy of interferon-alpha 2b and anlotinib in a patient with advanced hepatic epithelioid hemangioendothelioma.

Liu X, Zhou R, Si S, Liu L, Yang S, Han D Front Med (Lausanne). 2022; 9:1022017.

PMID: 36530920 PMC: 9755491. DOI: 10.3389/fmed.2022.1022017.

Sirolimus combined with interferon-alpha 2b therapy for giant hepatic epithelioid hemangioendothelioma: a case report.

Liu X, Zhou R, Si S, Liu L, Yang S, Han D Front Oncol. 2022; 12:972306.

PMID: 36081563 PMC: 9447363. DOI: 10.3389/fonc.2022.972306.

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