Synovial Sarcoma of Kidney in a Child: A Rare Presentation

Overview

Journal J Indian Assoc Pediatr Surg

Specialty Pediatrics

Date 2016 Apr 6

PMID 27046979

Citations 6

Authors

Venkatraman Radhakrishnan

Manikandan Dhanushkodi

Kathiresan Narayanswamy

Anand Raja

Shirley Sundersingh

Tenali Sagar

Affiliations

Soon will be listed here.

Abstract

There are no reported cases in the literature of primary renal synovial sarcoma in pediatric patients. The management of renal synovial sarcoma has been extrapolated from the management of soft tissue sarcomas at other sites. We present a 4-year-old female who was suspected to have Wilms' tumor. The patient underwent guided biopsy as she did not respond to neoadjuvant chemotherapy for Wilms' tumor. The biopsy was consistent with primary renal synovial sarcoma. The child was treated with change in her neoadjuvant chemotherapy regimen and surgery. The diagnosis of synovial sarcoma was confirmed by demonstrating the t (X, 18) translocation using polymerase chain reaction.

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