Arthrogryposis: an Update on Clinical Aspects, Etiology, and Treatment Strategies

Overview

Journal Arch Med Sci

Specialty General Medicine

Date 2016 Mar 1

PMID 26925114

Citations 29

Authors

Bartlomiej Kowalczyk

Jaroslaw Felus

Affiliations

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Abstract

Arthrogryposes - multiple joint contractures - are a clinically and etiologically heterogeneous class of diseases, where accurate diagnosis, recognition of the underlying pathology and classification are of key importance for the prognosis as well as for selection of appropriate management. This treatment remains challenging and optimally in arthrogrypotic patients should be carried out by a team of specialists familiar with all aspects of arthrogryposis pathology and treatment modalities: rehabilitation, orthotics and surgery. In this comprehensive review article, based on literature and clinical experience, the authors present an update on current knowledge on etiology, classifications and treatment options for skeletal deformations possible in arthrogryposis.

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