Chordoma in Children: Case-report and Review of Literature

Overview

Journal Rep Pract Oncol Radiother

Specialty Oncology

Date 2016 Feb 23

PMID 26900351

Citations 5

Authors

Jean-Louis Habrand

Jean Datchary

Stephanie Bolle

Anne Beaudre

Ludovic De Marzi

Kevin Beccaria

Dinu Stefan

Jacques Grill

Remi Dendale

Affiliations

Soon will be listed here.

Abstract

We report an exceptional case of a very late local failure in a 9-year-old boy presenting with a chordoma of the cranio-cervical junction. The child was initially treated with a combination of surgical resection followed by high dose photon-proton radiation therapy. This aggressive therapy allowed a 9-year remission with minimal side-effects. Unfortunately, he subsequently presented with a local failure managed with a second full-dose course of protons. The child died one year later from local bleeding of unclear etiology.

Citing Articles

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Characteristics and overall survival in pediatric versus adult skull base chordoma: a population-based study.

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Chordoma with lung metastases at initial presentation of a pediatric patient.

Agunbiade S, Nada A, Bhimaniya S, Whitehead M, Mahdi E Radiol Case Rep. 2020; 15(4):382-386.

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