Update on Diagnosis and Treatment of Idiopathic Pulmonary Fibrosis

Overview

Journal J Bras Pneumol

Specialty Pulmonary Medicine

Date 2015 Nov 19

PMID 26578138

Citations 18

Authors

Jose Baddini-Martinez

Bruno Guedes Baldi

Claudia Henrique da Costa

Sergio Jezler

Mariana Silva Lima

Rogerio Rufino

Affiliations

Soon will be listed here.

Abstract

Idiopathic pulmonary fibrosis is a type of chronic fibrosing interstitial pneumonia, of unknown etiology, which is associated with a progressive decrease in pulmonary function and with high mortality rates. Interest in and knowledge of this disorder have grown substantially in recent years. In this review article, we broadly discuss distinct aspects related to the diagnosis and treatment of idiopathic pulmonary fibrosis. We list the current diagnostic criteria and describe the therapeutic approaches currently available, symptomatic treatments, the action of new drugs that are effective in slowing the decline in pulmonary function, and indications for lung transplantation.

Citing Articles

Idiopathic pulmonary fibrosis: current diagnosis and treatment.

Amaral A, Colares P, Kairalla R J Bras Pneumol. 2023; 49(4):e20230085.

PMID: 37556670 PMC: 10578906. DOI: 10.36416/1806-3756/e20230085.

Antifibrotic therapy in idiopathic pulmonary fibrosis candidates for lung transplantation undergoing pulmonary rehabilitation.

Pereira M, Branchini G, Nunes F, Altmayer S, Hetzel G, Romero I J Bras Pneumol. 2023; 49(1):e20220250.

PMID: 36753211 PMC: 9970374. DOI: 10.36416/1806-3756/e20220250.

Radiographic Progression and Survival of the Different HRCT Patterns of Idiopathic Pulmonary Fibrosis.

Mura M, Rellini C, Taha N, Sbordone F, Rufi F, Montesanto F Sarcoidosis Vasc Diffuse Lung Dis. 2022; 39(2):e2022021.

PMID: 36118536 PMC: 9437754. DOI: 10.36141/svdld.v39i2.12534.

Combination Therapy of Wuweizi () and Dexamethasone Alleviated Dexamethasone-Induced Glucocorticoid Osteoporosis in Rats with Idiopathic Pulmonary Fibrosis.

Qin Z, Li S, Zhang X, Liu G, Gu M, Zhang N Biomed Res Int. 2020; 2020:6301697.

PMID: 32280693 PMC: 7115146. DOI: 10.1155/2020/6301697.

Brazilian guidelines for the pharmacological treatment of idiopathic pulmonary fibrosis. Official document of the Brazilian Thoracic Association based on the GRADE methodology.

Baddini-Martinez J, Ferreira J, Tanni S, Alves L, Cabral Junior B, Carvalho C J Bras Pneumol. 2020; 46(2):e20190423.

PMID: 32130337 PMC: 7462709. DOI: 10.36416/1806-3756/e20190423.

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