Cerebral Involvement in IgG4-related Disease

Overview

Journal Clin Med (Lond)

Specialty General Medicine

Date 2015 Apr 1

PMID 25824063

Citations 15

Authors

Deepak Joshi

Rolf Jager

Steven Hurel

Stephen P Pereira

Gavin J Johnson

Michael Chapman

Robert Fowler

Alison Winstanley

Nicholas Losseff

George Jm Webster

Affiliations

Soon will be listed here.

Abstract

IgG4-related disease is a recently recognised multi-system disease. Common organ involvement includes the pancreas, biliary tree and salivary glands. Central nervous system involvement has been infrequently reported. In a single-centre cohort of 84 patients, we report cerebral involvement in three (4%) patients. Details of cerebral involvement in these patients are outlined, including pituitary involvement in two patients and a diffuse autoimmune-like encephalopathy in the other.

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