Alternative Treatment for Open Bite Class III Malocclusion in a Child with Williams-Beuren Syndrome

Overview

Journal Dental Press J Orthod

Specialty Dentistry

Date 2015 Mar 6

PMID 25741831

Citations 2

Authors

Giovanni Modesto Vieira

Eduardo Jacomino Franco

Denise Falcao Pinheiro da Rocha

Laudimar Alves de Oliveira

Rivadavio Fernandes Batista Amorim

Affiliations

Soon will be listed here.

Abstract

Williams-Beuren syndrome (WBS) is a rare genetic condition that affects approximately 1 in every 20,000 - 50,000 live births. WBS children have specific skeletal deformities, dental malformations and rare lingual muscle dysfunction. The need for orthodontic and orthognathic therapy has arisen and has been considered a real clinical challenge even for experienced professionals, once it requires a complex and individualized treatment plan. This study reports a case of orthopedic expansion of the maxilla, in which a modified facial mask was used for protraction of the maxillary complex associated with clockwise rotation of the maxilla. In addition, special considerations about treatment time and orthopedic outcomes are discussed.

Citing Articles

Oral findings in Williams-Beuren syndrome.

Ferreira S, Viana M, Maia N, Leao L, Machado R, Coletta R Med Oral Patol Oral Cir Bucal. 2017; 23(1):e1-e6.

PMID: 29274148 PMC: 5822531. DOI: 10.4317/medoral.21834.

Orthodontic Treatment and Maxillary Anterior Segmental Distraction Osteogenesis of a Subject with Williams-Beuren Syndrome and Isolated Cleft Palate: A Long-Term Follow-Up from the Age of 5 to 24 Years.

Yamaguchi T, Shirota T, Adel M, Takahashi M, Haga S, Nagahama R Case Rep Dent. 2017; 2017:7019045.

PMID: 28744380 PMC: 5514341. DOI: 10.1155/2017/7019045.

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