Mesenteric Fibromatosis

Overview

Journal Int J Colorectal Dis

Specialties Gastroenterology
General Surgery

Date 2014 Aug 21

PMID 25139370

Citations 17

Authors

Poras Chaudhary

Affiliations

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Abstract

Mesenteric fibromatosis is a rare, locally invasive, non-metastasizing type of intra-abdominal fibromatoses with a very high rate of recurrence. Because of rarity, these tumors pose a diagnostic and therapeutic challenge. These tumors may remain asymptomatic, but commonly present as a painless mass. There are no clear treatment guidelines. Surgical excision with wide margin is the preferred modality of treatment. Medical therapy is indicated for inoperable and recurrent tumors. There are several isolated case reports on mesenteric fibromatosis with different and unusual presentations and its complications. Though several studies have been published on extra-abdominal fibromatosis as well as on extramesenteric abdominal fibromatosis, but extensive research studies are still lacking on mesenteric fibromatosis. The aim of this article is to present current knowledge on mesenteric fibromatosis, our experience of four cases, and comprehensive review of available literature.

Citing Articles

Solitary mesenteric fibromatosis in a male patient: clinical case report.

David Aulestia J, Piedra J, Ribadeneira A, Remache V, Vasconez C, Arias G J Surg Case Rep. 2023; 2023(5):rjad240.

PMID: 37192873 PMC: 10182391. DOI: 10.1093/jscr/rjad240.

Giant desmoid tumour mimicking recurrent uterine myoma in a nulliparous young Nigerian: a case report.

Njoku O, Umezurike C J Med Case Rep. 2022; 16(1):319.

PMID: 36028896 PMC: 9419363. DOI: 10.1186/s13256-022-03558-6.

A Giant Sporadic Intra-abdominal Desmoid Tumor in a Male Patient: A Case Report.

Elhaddad B, Gopireddy D, Liu S Cureus. 2022; 14(7):e26633.

PMID: 35949762 PMC: 9356662. DOI: 10.7759/cureus.26633.

Sporadic intra-abdominal desmoid tumor with a very unusual onset: two case reports.

Kuwabara H, Katayanagi S, Koganezawa I, Nakagawa M, Katsumata K, Tsuchida A J Med Case Rep. 2021; 15(1):457.

PMID: 34526110 PMC: 8444561. DOI: 10.1186/s13256-021-03058-z.

Transverse colonic volvulus due to mesenteric fibromatosis: a case report.

Yoshida A, Uchima Y, Hosaka N, Minaga K, Kudo M BMC Gastroenterol. 2021; 21(1):11.

PMID: 33407154 PMC: 7788689. DOI: 10.1186/s12876-020-01592-6.

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