Diagnosis and Treatment of Endocrine Comorbidities in Patients with Cystic Fibrosis

Overview

Journal Curr Opin Endocrinol Diabetes Obes

Specialty Endocrinology

Date 2014 Aug 9

PMID 25105995

Citations 16

Authors

Oranan Siwamogsatham

Jessica A Alvarez

Vin Tangpricha

Affiliations

Soon will be listed here.

Abstract

Purpose Of Review: The aim of this review is to provide an update on various relevant endocrine aspects of care in adolescents and adults with cystic fibrosis.

Recent Findings: As life expectancy in cystic fibrosis has continuously improved, endocrine complications have become more apparent. The common endocrine complications include cystic fibrosis related diabetes, cystic fibrosis related bone disease, vitamin D deficiency and poor growth and pubertal development. Thyroid and adrenal disorders have also been reported, although the prevalence appears to be less common.

Summary: Endocrine diseases are an increasingly recognized complication that has a significant impact on the overall health of individuals with cystic fibrosis. This review summarizes the updated screening and management of endocrine diseases in the cystic fibrosis population.

Citing Articles

Metabolomics Panel Associated with Cystic Fibrosis-Related Diabetes toward Biomarker Discovery.

Mujammami M, Nimer R, Al Mogren M, AlMalki R, Alabdaljabar M, Benabdelkamel H ACS Omega. 2024; 9(30):32873-32880.

PMID: 39100315 PMC: 11292812. DOI: 10.1021/acsomega.4c03626.

Vitamin D deficiency in patients with cystic fibrosis: a systematic review and meta-analysis.

Farahbakhsh N, Fatahi S, Shirvani A, Motaharifard M, Mohkam M, Tabatabaii S J Health Popul Nutr. 2024; 43(1):11.

PMID: 38233891 PMC: 10795301. DOI: 10.1186/s41043-024-00499-2.

Hope in Every Breath: Navigating the Therapeutic Landscape of Cystic Fibrosis.

Sreenivasulu H, Muppalla S, Vuppalapati S, Shokrolahi M, Reddy Pulliahgaru A Cureus. 2023; 15(8):e43603.

PMID: 37719614 PMC: 10504422. DOI: 10.7759/cureus.43603.

Predicting glycemic control status and high blood glucose levels through voice characteristic analysis in patients with cystic fibrosis-related diabetes (CFRD).

Suppakitjanusant P, Kasemkosin N, Sivapiromrat A, Weinstein S, Ongphiphadhanakul B, Hunt W Sci Rep. 2023; 13(1):8617.

PMID: 37244957 PMC: 10220341. DOI: 10.1038/s41598-023-35416-w.

MicroRNA global profiling in cystic fibrosis cell lines reveals dysregulated pathways related with inflammation, cancer, growth, glucose and lipid metabolism, and fertility: an exploratory study.

Catellani C, Cirillo F, Graziano S, Montanini L, Marmiroli N, Gulli M Acta Biomed. 2022; 93(3):e2022133.

PMID: 35775757 PMC: 9335447. DOI: 10.23750/abm.v93i3.12842.

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