Ganglioneuroma of the Internal Auditory Canal Presenting As a Vestibular Schwannoma

Overview

Journal Skull Base Rep

Date 2013 Aug 29

PMID 23984208

Citations 3

Authors

Kimon Bekelis

Duncan A Meiklejohn

Symeon Missios

Brent Harris

James E Saunders

Kadir Erkmen

Affiliations

Soon will be listed here.

Abstract

In most series, 90% of cerebellopontine angle tumors are vestibular schwannomas. Meningiomas and epidermoid tumors follow with decreased frequency. Ganglioneuroma is a benign tumor usually found in the retroperitoneum and posterior mediastinum. We report a case of a 21-year-old man with gradual sensorineural hearing loss and a minimally enhancing lesion of the internal auditory canal, which was excised through a middle fossa approach and found histologically to be a ganglioneuroma. Like vestibular schwannomas, these lesions are benign in nature and may be managed in a similar fashion, although the possibility of malignant transformation may support surgical resection over conservative management or radiosurgery. Ganglioneuromas should be considered in patients with atypical radiographic findings for vestibular schwannomas.

Citing Articles

An intracranial odyssey: pediatric ganglioneuroma arising from the trigeminal ganglion: a case report and review of the literature.

Ebrahimzadeh K, Eraghi M, Bidari Zerehpoosh F, Tavasol H, Abbaszdeh M, Dmytriw A J Med Case Rep. 2024; 18(1):600.

PMID: 39695863 PMC: 11654053. DOI: 10.1186/s13256-024-04947-9.

Invasive trigeminal ganglioneuroma: A case report and review of the literature.

Narra R, Are K, Nuzhat P Acta Radiol Open. 2024; 13(9):20584601241283780.

PMID: 39257594 PMC: 11384535. DOI: 10.1177/20584601241283780.

Ganglioneuroma of the External Auditory Canal and Middle Ear.

Almofada H, Timms M, Dababo M Case Rep Otolaryngol. 2017; 2017:4736895.

PMID: 28875046 PMC: 5569943. DOI: 10.1155/2017/4736895.

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