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Application of CRT-D in a Marfan Syndrome Patient with Chronic Heart Failure Accompanied by Ventricular Tachycardia and Ventricular Fibrillation

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Date 2013 Jul 31
PMID 23897797
Citations 2
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Abstract

Marfan syndrome is a systemic connective tissue disease that could affect the cardiovascular system and eventually lead to heart enlargement and heart failure with high mortality, mainly due to progressive heart failure and/or sudden cardiac death caused by malignant arrhythmia. Here we report that a patient received a cardiac resynchronization therapy-defibrillator (CRT-D) with a pre-monitor function for heart failure and experienced obvious improvements in his cardiac function. Postoperative follow-up showed that the patient had reduced morbidity and hospitalization for heart failure, and also experienced improved quality of life.

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References
1.
Chung E, Leon A, Tavazzi L, Sun J, Nihoyannopoulos P, Merlino J . Results of the Predictors of Response to CRT (PROSPECT) trial. Circulation. 2008; 117(20):2608-16. DOI: 10.1161/CIRCULATIONAHA.107.743120. View

2.
Penicka M, Bartunek J, De Bruyne B, Vanderheyden M, Goethals M, DE Zutter M . Improvement of left ventricular function after cardiac resynchronization therapy is predicted by tissue Doppler imaging echocardiography. Circulation. 2004; 109(8):978-83. DOI: 10.1161/01.CIR.0000116765.43251.D7. View

3.
Suffoletto M, Dohi K, Cannesson M, Saba S, Gorcsan 3rd J . Novel speckle-tracking radial strain from routine black-and-white echocardiographic images to quantify dyssynchrony and predict response to cardiac resynchronization therapy. Circulation. 2006; 113(7):960-8. DOI: 10.1161/CIRCULATIONAHA.105.571455. View

4.
Russo A, Sauer W, Gerstenfeld E, Hsia H, Lin D, Cooper J . Defibrillation threshold testing: is it really necessary at the time of implantable cardioverter-defibrillator insertion?. Heart Rhythm. 2005; 2(5):456-61. DOI: 10.1016/j.hrthm.2005.01.015. View

5.
Baker 2nd J, McKenzie 3rd J, Beau S, Greer G, Porterfield J, Fedor M . Acute evaluation of programmer-guided AV/PV and VV delay optimization comparing an IEGM method and echocardiogram for cardiac resynchronization therapy in heart failure patients and dual-chamber ICD implants. J Cardiovasc Electrophysiol. 2007; 18(2):185-91. DOI: 10.1111/j.1540-8167.2006.00671.x. View