Mycobacterium Avium Complex-Associated Hemophagocytic Lymphohistiocytosis in a Sickle Cell Patient: An Unusual Fatal Association

Overview

Journal Case Rep Hematol

Publisher Wiley

Specialty Hematology

Date 2013 Jun 14

PMID 23762672

Citations 8

Authors

Mohammed A R Chamsi-Pasha

M Chadi Alraies

Abdul Hamid Alraiyes

Eric D Hsi

Affiliations

Soon will be listed here.

Abstract

Hemophagocytic lymphohistiocytosis (HLH) is a rare hyperinflammatory syndrome, characterized clinically by fever, splenomegaly, cytopenia, and high ferritin. Infectious causes have been associated with secondary HLH, with viruses being the most common. We report a case of Mycobacterium avium complex-associated HLH in a sickle cell anemia patient. To the best of our knowledge, this association has never been reported in sickle cell anemia.

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