Ciliary Body Medulloepithelioma in an Adult

A 67-year-old woman presented with complaints of poor vision and persistent redness in the right eye of 4 months duration. She had undergone an uncomplicated cataract surgery in the same eye 2 years ago and had regained visual acuity of 20/20 with a then otherwise unremarkable eye examination. She had only light perception in the affected right eye with an intraocular pressure of 42 mm Hg. There were dilated episcleral vessels inferotemporally. Powdery white material was dispersed over the corneal endothelium and in the anterior chamber. There was diffuse iris neovascularization and a large yellowish white, fluffy, ciliary body mass. A metastasis was suspected, but systemic evaluation failed to reveal a primary. In view of the neovascular glaucoma, poor visual potential, and suspicion of a malignancy, the eye was enucleated. Histopathological examination revealed malignant nonteratoid ciliary body medulloepithelioma. Although ciliary body medulloepithelioma is predominantly a pediatric tumor, this case emphasizes the need to include it in the differential diagnosis of ciliary body tumors in adults.