Can Behcet's Disease Related Pulmonary Arterial Aneurysms Be Completely Resolved?

Overview

Journal Open Rheumatol J

Publisher Bentham Open

Specialty Rheumatology

Date 2012 Jan 5

PMID 22216070

Citations 3

Authors

Adnan Agha

Abdelhaleem M E Bella

Al-Hussain M Assiri

Mohammad Al-Hakami

Affiliations

Soon will be listed here.

Abstract

Behçet disease is a systemic disease with diverse clinical symptoms which include, but not limited to, patients having oral and genital ulcers and eye involvement. We here report an 18-year-old male presenting with massive hemoptysis and cardiac arrest, having history of ulcers in the oral cavity and genitalia as well as having recent episode of uveitis. A pulmonary CT angiography revealed bilateral arterial aneurysms of pulmonary vessels. On receiving Immunosuppressive treatment for Behcet disease with prednisone and azathioprine over one year the pulmonary arterial aneurysms were completely resolved and the patient was discharged from the hospital albeit with persistent hypoxic brain injury from cardiac arrest.

Citing Articles

Pulmonary vasculitis in Behçet's disease: reference atlas computed tomography pulmonary angiography (CTPA) findings and risk assessment-management proposal.

Emad Y, Ragab Y, Cozzi D, Ibrahim O, Abdelrahman W, Abdelali M Sarcoidosis Vasc Diffuse Lung Dis. 2023; 40(3):e2023026.

PMID: 37712377 PMC: 10540716. DOI: 10.36141/svdld.v40i3.13726.

An Adolescent Presented With Hemoptysis: Pulmonary Artery Aneurysm in Pediatric Behçet's Disease.

Bas Ikizoglu N, Atag E, Ergenekon A, Yilmaz Yegit C, Gokdemir Y, Erdem Eralp E Arch Rheumatol. 2020; 35(2):283-286.

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Behçet's disease leaves the silk road.

Wozniacka A, Jurowski P, Omulecki A, Kot M, Dziankowska-Bartkowiak B Postepy Dermatol Alergol. 2015; 31(6):417-20.

PMID: 25610360 PMC: 4293383. DOI: 10.5114/pdia.2014.40943.

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