A to Z of Extraskeletal Ewing Sarcoma Family of Tumors in Adults: Imaging Features of Primary Disease, Metastatic Patterns, and Treatment Responses

Overview

Journal AJR Am J Roentgenol

Specialties Oncology
Radiology

Date 2011 Nov 24

PMID 22109315

Citations 57

Authors

Omar Javery

Katherine Krajewski

Kevin ORegan

Bela Kis

Angela Giardino

Jyothi Jagannathan

Nikhil H Ramaiya

Affiliations

Soon will be listed here.

Abstract

Objective: Though classically thought of as an osseous-based sarcoma of children and adolescents, it is important to recognize that approximately 20% of all cases of Ewing sarcoma family of tumors (ESFT) occur in patients older than 18 years, often with extraskeletal disease. Understanding the specific imaging features, manners of presentation, and patterns of behavior of ESFT is therefore important in all settings.

Conclusion: This article presents the imaging findings of ESFT in the adult, with specific attention to extraskeletal manifestations.

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