Cystic Appearance of Low-grade Endometrial Stromal Sarcoma in the Right Atrium: Case Report

Overview

Journal Cardiovasc Ultrasound

Publisher Biomed Central

Specialties Cardiology & Vascular Diseases
Radiology

Date 2011 Aug 26

PMID 21864385

Citations 2

Authors

Cristina L Wood

James Sederberg 2nd

Paul Russ

Tamas Seres

Affiliations

Soon will be listed here.

Abstract

A 71-year-old woman presented with a right adnexal solid mass invading the right gonadal vein and inferior vena cava up to the hepatic veins revealed by CT and confirmed by MRI. A thin-walled cyst and a solid mass were unexpectedly found in the right atrium by transesophageal echocardiography (TEE) in the operating room. Using color Doppler and air bubbles as contrast material a circumscribed cyst was confirmed and localized close to the IVC. The cyst was connected to the mass in the inferior vena cava. The tumor, including the cyst, was removed without using cardiopulmonary bypass and described as a low-grade endometrial stromal sarcoma, a rare slowly growing tumor. This is the first TEE description of endometrial stromal sarcoma manifesting as a right atrial cyst.

Citing Articles

Case Report: Low-grade endometrial stromal sarcoma with intravenous and intracardiac extension: a case after misdiagnosis of endometrial stromal nodule as submucosal fibroid.

Chai X, Tao G, Ding H, Zhou P, Mei X, Li X Front Oncol. 2023; 13:1205783.

PMID: 37909010 PMC: 10613730. DOI: 10.3389/fonc.2023.1205783.

Ultrasonographic findings of low-grade endometrial stromal sarcoma of the uterus with a focus on cystic degeneration.

Park G, Eun Rha S, Oh S, Lee A, Lee K, Kim M Ultrasonography. 2015; 35(2):124-30.

PMID: 26537303 PMC: 4825207. DOI: 10.14366/usg.15045.

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