Successful Surgical Excision of Primary Right Atrial Angiosarcoma

Overview

Journal J Cardiothorac Surg

Publisher Biomed Central

Specialties Cardiology & Vascular Diseases
General Surgery
Pulmonary Medicine

Date 2011 Apr 12

PMID 21477334

Citations 16

Authors

Wobbe Bouma

Chris P H Lexis

Tineke P Willems

Albert J H Suurmeijer

Iwan C C van der Horst

Tjark Ebels

Massimo A Mariani

Affiliations

Soon will be listed here.

Abstract

Primary cardiac angiosarcoma is a rare and aggressive tumor with a high incidence of metastatic spread (up to 89%) at the time of diagnosis, which restricts the indication for surgical resection to a small number of patients. We report the case of a 50-year old Caucasian woman with non-metastatic primary right atrial angiosarcoma, who underwent successful surgical excision of the tumor (with curative intent) and reconstruction of the right atrium with a porcine pericardial patch. However, after a symptom-free survival of five months the patient presented with bone and liver metastases without evidence of local tumor recurrence.

Citing Articles

Rapid Development of Primary Right Atrial Angiosarcoma.

Talbot S, Bandaru V, Nguyen T, Arif D, Sethi P Cureus. 2024; 16(7):e64273.

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Long-Term Efficacy Analysis of Surgical Resection of 70 Primary Right Heart Tumors.

Li T, Zhang S, Liu C, Peng X, Gong S, Pan W Cardiology. 2024; 149(2):147-154.

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Case Report: Successful surgical management of a challenging primary cardiac angiosarcoma.

Li Y, Ai Y, Tang W, Liu J, Yang J, Fan C Front Cardiovasc Med. 2023; 10:1279177.

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Survival and analysis of prognostic factors for primary malignant cardiac tumors based on the SEER database.

Chen X, Chen Y, Xiao F, Liu M, Gu Z, Li Y J Cancer Res Clin Oncol. 2023; 149(17):15687-15696.

PMID: 37665405 DOI: 10.1007/s00432-023-05351-4.

Right atrium angiosarcoma with feeding vessels from right coronary artery: a case report.

Yeh J, Tsai Y, Chen Y, Roan J, Chang H Eur Heart J Case Rep. 2022; 6(1):ytac025.

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